Neurological manifestations of Erdheim-Chester disease
نویسندگان
چکیده
منابع مشابه
Neurological manifestations in Erdheim-Chester disease: Two case reports.
Erdheim-Chester disease (ECD) is a rare form of non-Langerhans cell histiocytosis characterised by multiorgan xanthogranulomatous infiltration of histiocytes (CD68+/CD1−). Two highly suggestive characteristics of this disease are sclerosis of the long bones and perirenal fat infiltration. The central nervous system (CNS) involvement occurs in 30% to 50% of cases and is the main predictor of a p...
متن کاملSHORT REPORT Neurological manifestations of Erdheim-Chester disease
Erdheim-Chester disease is a rare sporadic systemic histiocytic disease of unknown aetiology that aVects multiple organ systems. The case records of all patients with Erdheim-Chester disease who had been seen at the Mayo Clinic between 1975 and 1996 were reviewed to assess the neurological manifestations of the disease. Two of 10 patients had neurological involvement. A 42 year old woman develo...
متن کاملMultisystem Radiologic Manifestations of Erdheim-Chester Disease
Erdheim-Chester Disease is a rare form of multiorgan non-Langerhans' cell histiocytosis that affects individuals between the ages of 50 and 70 with an equal distribution among males and females. It is associated with significant morbidity and mortality that is mostly due to infiltration of critical organs. Some of the sites that Erdheim-Chester Disease affects include the skeletal system, centr...
متن کاملErdheim-Chester Disease
Erdheim-Chester disease (ECD) is a rare, xanthogranulomatous, non-Langerhans cell histiocytosis with frequent systemic involvement. Although the diagnosis is based on characteristic histological and radiological findings, its identification can be challenging because of its heterogeneous presentation. Osteosclerosis of long bones, often associated with bone pain, is the most common initial mani...
متن کاملErdheim-chester disease.
Erdheim-Chester disease (ECD) is a rare, non-Langerhans cell histiocytosis of unknown etiology, characterized by multi-organ involvement. ECD is usually diagnosed on the basis of characteristic radiologic and histopathological findings. Lesions may be skeletal and/or extraskeletal in location, and may include the skin, lung, heart, and central nervous system. We describe here a 68-year-old man ...
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ژورنال
عنوان ژورنال: Journal of Neurology, Neurosurgery & Psychiatry
سال: 1999
ISSN: 0022-3050
DOI: 10.1136/jnnp.66.1.72